Interruption of aortic arch. Case report
| dc.contributor.author | Mayor-Barrera, Adriana | |
| dc.contributor.author | Velásquez-Trujillo, Paula Andrea | |
| dc.contributor.author | Ramírez-Muñoz, Paula Andrea | |
| dc.contributor.author | Santacruz-Vargas, Darío Alberto | |
| dc.date | 2017-12-30 | |
| dc.description | Aortic arch interruption (IAA) is a relatively rare genetic disorder, usually associated with a non-restrictive ventricular septal defect (VSD) and ductus arteriosus or, to a lesser extent, a large aortopulmonary or truncus arteriosus window. It can coexist with any ventricle-arterial alignment and also with severe underdevelopment of a ventricle. The interrupted aortic arch and the complete common atrioventricular canal can be observed in the context of coloboma, heart disease, choana atresia, intrauterine growth restriction and / or Central Nervous System abnormalities. Approximately 50% of patients with interrupted aortic arch have DiGeorge syndrome; In these cases, the interrupted aortic arch is usually type B, although cases of type A or type C have also been reported. Because the aortic arch and associated cardiac abnormalities represent a neonatal surgical emergency, the therapeutic plan consists of the Treatment for biventricular failure and infusion of PGE 1 to maintain ductal permeability and surgical correction as soon as possible. | en-US |
| dc.description | La interrupción del arco aórtico (IAA), es un trastorno genético relativamente raro, ocurre generalmente asociado a un defecto septal ventricular no restrictivo (VSD) y conducto arterioso o, en menor proporcion, con una gran ventana aortopulmonar o tronco arterioso. Puede coexistir con cualquier alineación ventrículo-arterial y también con un subdesarrollo severo de un ventrículo. El arco aórtico interrumpido y el canal auriculoventricular común completo se pueden observar en el contexto de coloboma, cardiopatía, atresia de coana, restricción de crecimiento intrauterino y/o anomalías del Sistema Nervioso Central. Aproximadamente el 50% de los pacientes con arco aórtico interrumpido tienen síndrome de DiGeorge; En estos casos, el arco aórtico interrumpido suele ser de tipo B, aunque también se han reportado casos de tipo A o tipo C. Debido a que el arco aórtico y las anomalías cardíacas asociadas representan una emergencia quirúrgica neonatal, el plan terapéutico consiste en el tratamiento para la falla biventricular y la infusión de PGE 1 para mantener la permeabilidad ductal y corrección quirúrgica lo antes posible. | es-ES |
| dc.format | application/pdf | |
| dc.identifier | https://revistas.unilibre.edu.co/index.php/rcslibre/article/view/1738 | |
| dc.identifier.uri | http://hdl.handle.net/10901/15045 | |
| dc.language | spa | |
| dc.language.iso | spa | spa |
| dc.publisher | Universidad Libre | es-ES |
| dc.relation | https://revistas.unilibre.edu.co/index.php/rcslibre/article/view/1738/1260 | |
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| dc.relation.ispartofjournal | Revistas - Ciencias de la Salud | spa |
| dc.rights.license | Atribución-NoComercial-SinDerivadas 2.5 Colombia | * |
| dc.rights.uri | http://creativecommons.org/licenses/by-nc-nd/2.5/co/ | * |
| dc.source | Revista Colombiana Salud Libre; Vol. 12 Núm. 2 (2017): Revista Colombiana Salud Libre; 67-70 | es-ES |
| dc.source | 2539-3340 | |
| dc.source | 1900-7841 | |
| dc.title | Interruption of aortic arch. Case report | en-US |
| dc.title | Interrupción del arco aórtico. Reporte de caso | es-ES |
| dc.type.coar | http://purl.org/coar/resource_type/c_6501 | |
| dc.type.coarversion | http://purl.org/coar/version/c_970fb48d4fbd8a85 |